| | MeSH | Disease Ontology |
| Disease ID: | D009072 | DOID:13099 |
| Disease Name: | Moyamoya disease | Moyamoya disease |
| Category: | MeSH | Disease Ontology |
| Type: | Nervous System Diseases//Cardiovascular Diseases | disease of anatomical entity//nervous system disease |
| Define: | A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults. | A cerebral arterial disease characterized by constriction of certain arteries at the base of the brain. Blood flow is blocked by the constriction and also by blood clots. |
| Alias: | Cerebrovascular Moyamoya Disease//Moya-Moya Disease//Moyamoya Disease, Classic//Moyamoya Disease, Primary//Moyamoya Disease, Secondary//Moyamoya Syndrome//Progressive Intracranial Occlusive Arteropathy (Moyamoya) | progressive intracranial arterial occlusion |